Anesthetic management of a patient with branchiooto-renal syndrome
Tsukamoto Masanori, Yokoyama Takeshi,
소속 상세정보
( Tsukamoto Masanori ) - Kyushu University Hospital Department of Dental Anesthesiology
( Yokoyama Takeshi ) - Kyushu University Faculty of Dental Science Department of Dental Anesthesiology
Abstract
Branchio-oto-renal syndrome (BOR) is a rare autosomal dominant disorder. The features include branchial cysts, hearing loss, ear malformation, preauricular pits, retrognathia, congenital heart disease, and renal abnormalities. However, anesthetic management of these patients has seldom been reported. We report a case in which general anesthesia was performed for dental treatment in a patient with BOR. Airway management, renal function, and hemodynamic changes can be of critical concern during anesthetic management. A 13-year-old girl diagnosed with BOR had severe right hearing loss, right external ear malformation, renal abnormalities, and postoperative patent ductus arteriosus (PDA). Dental extraction under general anesthesia was scheduled for a supernumerary tooth. The procedure was completed with sufficient urine volume, adequate airway management, and stable hemodynamics.
키워드
Branchio-oto-renal Syndrome; Congenital Heart Disease; Difficult Airway; General Anesthesia; Renal Failure
원문 및 링크아웃 정보
등재저널 정보